neonatal lethal pontocerebellar hypoplasia, hypotonia, and respiratory insufficiency syndrome

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A syndrome that is characterized in infants showing respiratory insufficiency and almost no spontaneous movement at birth, usually requiring mechanical ventilation and admission to the neonatal intensive care unit and that has_material_basis_in compound heterozygous mutation in the ATAD3A gene on chromosome 1p36.33. [ url:https://pubmed.ncbi.nlm.nih.gov/28549128/ ]

Synonyms: PHRINL syndrome

This is just here as a test because I lose it

Term information

database cross reference
  • ORDO:615983
  • MIM:618810
Subsets

DO_rare_slim

has obo namespace

disease_ontology

id

DOID:0081396